2bbs: Difference between revisions

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|PDB= 2bbs |SIZE=350|CAPTION= <scene name='initialview01'>2bbs</scene>, resolution 2.050&Aring;
|PDB= 2bbs |SIZE=350|CAPTION= <scene name='initialview01'>2bbs</scene>, resolution 2.050&Aring;
|SITE=  
|SITE=  
|LIGAND= <scene name='pdbligand=MG:MAGNESIUM+ION'>MG</scene> and <scene name='pdbligand=ATP:ADENOSINE-5&#39;-TRIPHOSPHATE'>ATP</scene>
|LIGAND= <scene name='pdbligand=ATP:ADENOSINE-5&#39;-TRIPHOSPHATE'>ATP</scene>, <scene name='pdbligand=MG:MAGNESIUM+ION'>MG</scene>
|ACTIVITY=  
|ACTIVITY=  
|GENE= CFTR, ABCC7 ([http://www.ncbi.nlm.nih.gov/Taxonomy/Browser/wwwtax.cgi?mode=Info&srchmode=5&id=9606 Homo sapiens])
|GENE= CFTR, ABCC7 ([http://www.ncbi.nlm.nih.gov/Taxonomy/Browser/wwwtax.cgi?mode=Info&srchmode=5&id=9606 Homo sapiens])
|DOMAIN=
|RELATEDENTRY=[[2bbo|2BBO]], [[2bbt|2BBT]]
|RESOURCES=<span class='plainlinks'>[http://oca.weizmann.ac.il/oca-docs/fgij/fg.htm?mol=2bbs FirstGlance], [http://oca.weizmann.ac.il/oca-bin/ocaids?id=2bbs OCA], [http://www.ebi.ac.uk/pdbsum/2bbs PDBsum], [http://www.rcsb.org/pdb/explore.do?structureId=2bbs RCSB]</span>
}}
}}


'''Human deltaF508 NBD1 with three solubilizing mutations'''
'''Human deltaF508 NBD1 with three solubilizing mutations'''


==Disease==
Known diseases associated with this structure: Congenital bilateral absence of vas deferens OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=602421 602421]], Cystic fibrosis OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=602421 602421]], Hypertrypsinemia, neonatal OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=602421 602421]], Pancreatitis, idiopathic OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=602421 602421]], Sweat chloride elevation without CF OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=602421 602421]]


==About this Structure==
==About this Structure==
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[[Category: Sauder, J M.]]
[[Category: Sauder, J M.]]
[[Category: Zhao, X.]]
[[Category: Zhao, X.]]
[[Category: ATP]]
[[Category: MG]]
[[Category: atp binding cassette]]
[[Category: atp binding cassette]]


''Page seeded by [http://oca.weizmann.ac.il/oca OCA ] on Sun Mar 23 14:43:36 2008''
''Page seeded by [http://oca.weizmann.ac.il/oca OCA ] on Mon Mar 31 02:04:06 2008''