2dob: Difference between revisions
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|PDB= 2dob |SIZE=350|CAPTION= <scene name='initialview01'>2dob</scene>, resolution 2.00Å | |PDB= 2dob |SIZE=350|CAPTION= <scene name='initialview01'>2dob</scene>, resolution 2.00Å | ||
|SITE= | |SITE= | ||
|LIGAND= <scene name='pdbligand=CA:CALCIUM ION'>CA</scene> | |LIGAND= <scene name='pdbligand=CA:CALCIUM+ION'>CA</scene>, <scene name='pdbligand=MSE:SELENOMETHIONINE'>MSE</scene> | ||
|ACTIVITY= | |ACTIVITY= | ||
|GENE= PSAP ([http://www.ncbi.nlm.nih.gov/Taxonomy/Browser/wwwtax.cgi?mode=Info&srchmode=5&id=9606 Homo sapiens]) | |GENE= PSAP ([http://www.ncbi.nlm.nih.gov/Taxonomy/Browser/wwwtax.cgi?mode=Info&srchmode=5&id=9606 Homo sapiens]) | ||
|DOMAIN= | |||
|RELATEDENTRY=[[1n69|1N69]], [[1m12|1M12]], [[2gtg|2GTG]] | |||
|RESOURCES=<span class='plainlinks'>[http://oca.weizmann.ac.il/oca-docs/fgij/fg.htm?mol=2dob FirstGlance], [http://oca.weizmann.ac.il/oca-bin/ocaids?id=2dob OCA], [http://www.ebi.ac.uk/pdbsum/2dob PDBsum], [http://www.rcsb.org/pdb/explore.do?structureId=2dob RCSB]</span> | |||
}} | }} | ||
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==Disease== | ==Disease== | ||
Known | Known disease associated with this structure: Combined SAP deficiency OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=176801 176801]], Gaucher disease, atypical OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=176801 176801]], Krabbe disease, atypical OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=176801 176801]], Metachromatic leukodystrophy due to SAP-b deficiency OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=176801 176801]] | ||
==About this Structure== | ==About this Structure== | ||
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[[Category: Ahn, V E.]] | [[Category: Ahn, V E.]] | ||
[[Category: Prive, G G.]] | [[Category: Prive, G G.]] | ||
[[Category: lipid-binding protein]] | [[Category: lipid-binding protein]] | ||
[[Category: saposin]] | [[Category: saposin]] | ||
[[Category: sphingolipid activator protein]] | [[Category: sphingolipid activator protein]] | ||
''Page seeded by [http://oca.weizmann.ac.il/oca OCA ] on | ''Page seeded by [http://oca.weizmann.ac.il/oca OCA ] on Mon Mar 31 02:37:19 2008'' | ||