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| Line 4: |
Line 4: |
| |PDB= 2hbd |SIZE=350|CAPTION= <scene name='initialview01'>2hbd</scene>, resolution 2.2Å | | |PDB= 2hbd |SIZE=350|CAPTION= <scene name='initialview01'>2hbd</scene>, resolution 2.2Å |
| |SITE= | | |SITE= |
| |LIGAND= <scene name='pdbligand=HEM:PROTOPORPHYRIN+IX+CONTAINING+FE'>HEM</scene> and <scene name='pdbligand=MNC:METHYL ISOCYANIDE'>MNC</scene> | | |LIGAND= <scene name='pdbligand=HEM:PROTOPORPHYRIN+IX+CONTAINING+FE'>HEM</scene>, <scene name='pdbligand=MNC:METHYL+ISOCYANIDE'>MNC</scene> |
| |ACTIVITY= | | |ACTIVITY= |
| |GENE= | | |GENE= |
| | |DOMAIN= |
| | |RELATEDENTRY= |
| | |RESOURCES=<span class='plainlinks'>[http://oca.weizmann.ac.il/oca-docs/fgij/fg.htm?mol=2hbd FirstGlance], [http://oca.weizmann.ac.il/oca-bin/ocaids?id=2hbd OCA], [http://www.ebi.ac.uk/pdbsum/2hbd PDBsum], [http://www.rcsb.org/pdb/explore.do?structureId=2hbd RCSB]</span> |
| }} | | }} |
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| '''HIGH RESOLUTION X-RAY STRUCTURES OF MYOGLOBIN-AND HEMOGLOBIN-ALKYL ISOCYANIDE COMPLEXES''' | | '''HIGH RESOLUTION X-RAY STRUCTURES OF MYOGLOBIN-AND HEMOGLOBIN-ALKYL ISOCYANIDE COMPLEXES''' |
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| ==Disease==
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| Known diseases associated with this structure: Erythremias, alpha- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141800 141800]], Erythremias, beta- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141900 141900]], Erythrocytosis OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141850 141850]], HPFH, deletion type OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141900 141900]], Heinz body anemia OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141850 141850]], Heinz body anemias, alpha- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141800 141800]], Heinz body anemias, beta- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141900 141900]], Hemoglobin H disease OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141850 141850]], Hypochromic microcytic anemia OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141850 141850]], Methemoglobinemias, alpha- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141800 141800]], Methemoglobinemias, beta- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141900 141900]], Sickle cell anemia OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141900 141900]], Thalassemia, alpha- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141850 141850]], Thalassemia-beta, dominant inclusion-body OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141900 141900]], Thalassemias, alpha- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141800 141800]], Thalassemias, beta- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141900 141900]]
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| ==About this Structure== | | ==About this Structure== |
| Line 22: |
Line 22: |
| [[Category: Jr., G N.Phillips.]] | | [[Category: Jr., G N.Phillips.]] |
| [[Category: Olson, J S.]] | | [[Category: Olson, J S.]] |
| [[Category: HEM]]
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| [[Category: MNC]]
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| [[Category: oxygen transport]] | | [[Category: oxygen transport]] |
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| ''Page seeded by [http://oca.weizmann.ac.il/oca OCA ] on Thu Mar 20 17:14:58 2008'' | | ''Page seeded by [http://oca.weizmann.ac.il/oca OCA ] on Mon Mar 31 03:28:05 2008'' |