1olx | pdb_00001olx
From Proteopedia
ROLES OF HIS291-ALPHA AND HIS146-BETA' IN THE REDUCTIVE ACYLATION REACTION CATALYZED BY HUMAN BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE
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Disease
Known diseases associated with this structure: Maple syrup urine disease, type Ia OMIM:[608348], Maple syrup urine disease, type Ib OMIM:[248611]
About this Structure
1OLX is a Protein complex structure of sequences from Homo sapiens with K, MN, TDP and GOL as ligands. Active as 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring), with EC number 1.2.4.4 Known structural/functional Site: KA. Full crystallographic information is available from OCA.
Page seeded by OCA on Sun Feb 3 09:59:38 2008
Proteopedia Page Contributors and Editors (what is this?)
Categories:
- Pages with broken file links
- 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
- Homo sapiens
- Protein complex
- Chuang, D.T.
- Chuang, J.L.
- Li, J.
- Machius, M.
- Tomchick, D.R.
- Wynn, R.M.
- GOL
- K
- MN
- TDP
- Acylation
- Branched-chain
- Ketoacid dehydrogenase
- Maple syrup urine disease
- Multi-enzyme complex
- Oxidative decarboxylation oxidoreductase
- Thiamine phosphate
