Propionyl-CoA carboxylase

spinqualitylabelsall models Caption for this structure Show:Asymmetric Unit Biological Assembly Drag the structure with the mouse to rotate   Export Animated Image   Print3D Function Propionyl-CoA carboxylase (PCC) is a biotin-dependent enzyme that catalyzes the conversion of propionyl-CoA to D-methylmalonyl-CoA. PCC is composed of two subunits - α and β. The β subunit is the carboxyltransferase subunit. See also 3-Hydroxypropionate_bicycle. Disease Mutations in the β subunit cause PCC deficiency resulting in the metabolic disorder - propionic acidemia. Structural highlights This is a sample scene created with SAT to color by Group, and another to make a transparent representation of the protein. You can make your own scenes on SAT starting from scratch or loading and editing one of these sample scenes.

Proteopedia Page Contributors and Editors (what is this?)

Michal Harel, Alexander Berchansky